CYSTIC ADENOMATOID MALFORMATION OF LUNG
Last Updated : 4/5/2010
Dr. Ira Shah
More..
What is

cystic adenomatoid malformation

?

It is a birth defect of the lung characterized by cysts in the lung since birth leading to difficulty in breathing (respiratory distress) right from the first day of life.

What are the

signs and symptoms of cystic adenomatoid malformation

?

Most of the newborns present with respiratory distress at time of birth. A few may have indolent respiratory infections with chronic cough. Some children may have generalized body swelling, pneumonia or intestinal obstruction associated with it.

What is the

cause of cystic adenomatoid malformation

?

The abnormal development occurs in the baby when in the mother's womb. Adenomatoid (normal tissue but put together improperly) overgrowth of lung tissue leads to this situation. The reason for the abnormal development is still not known.

How is the

diagnosis of cystic adenomatoid malformation

made?

An X-Ray Chest usually detects the malformation in majority of patients. CT or MRI of the chest may be required to exclude other conditions that may mimic cystic adenomatoid malformation. Chest X-Ray and CT may show large masses containing multiple, large thin walled cysts.

What is the

treatment for cystic adenomatoid malformation

?

Patients with severe respiratory distress may require artificial ventilation with ventilators to maintain oxygen supply to the body. Corrective surgery in form of removal of the malformed mass or the affected lung (lobectomy) may be required.



Contributor Information and Disclosures

Dr. Ira Shah
Consultant Pediatrician, B.J.Wadia Hospital for Children, Mumbai, India


First Created : 2/5/2001

References

Disclaimer: The information given by www.pediatriconcall.com is provided by medical and paramedical & Health providers voluntarily for display & is meant only for informational purpose. The site does not guarantee the accuracy or authenticity of the information. Use of any information is solely at the user's own risk. The appearance of advertisement or product information in the various section in the website does not constitute an endorsement or approval by Pediatric Oncall of the quality or value of the said product or of claims made by its manufacturer.